Patients with advanced variants of Systemic Mastocytosis may develop destructive bone lesions when massive mast cell (MC) infiltrates are present. Finding of large osteolyses in indolent systemic mastocytosis, typically characterized by low MC burden, should prompt investigations for an alternative explanation.

Multiple large osteolytic lesions in a patient with systemic mastocytosis: a challenging diagnosis

Zamò, Alberto;
2017-01-01

Abstract

Patients with advanced variants of Systemic Mastocytosis may develop destructive bone lesions when massive mast cell (MC) infiltrates are present. Finding of large osteolyses in indolent systemic mastocytosis, typically characterized by low MC burden, should prompt investigations for an alternative explanation.
2017
5
12
1988
1991
Non‐hodgkin lymphoma; osteolysis; primary bone lymphoma; systemic mastocytosis; tryptase
Bonifacio, Massimiliano; Zanotti, Roberta; Guardalben, Emanuele; Mimiola, Elda; Scognamiglio, Francesca; Perbellini, Omar; De Matteis, Giovanna; Escribano, Luis; Bonadonna, Patrizia; Grigolato, Daniela; Bissoli, Sergio; Parisi, Alice; Zamò, Alberto; Ambrosetti, Achille; Rossini, Maurizio
File in questo prodotto:
File Dimensione Formato  
Bonifacio_et_al-2017-Clinical_Case_Reports.pdf

Accesso aperto

Tipo di file: PDF EDITORIALE
Dimensione 1.44 MB
Formato Adobe PDF
1.44 MB Adobe PDF Visualizza/Apri

I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.

Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/2318/1671218
Citazioni
  • ???jsp.display-item.citation.pmc??? 3
  • Scopus ND
  • ???jsp.display-item.citation.isi??? 3
social impact