TEMPIA, Filippo
TEMPIA, Filippo
NEUROSCIENZE "RITA LEVI MONTALCINI"
A NOVEL GENE FOR SPINOCEREBELLAR ATAXIA (SCA) LINKED TO CHROMOSOME 6 AND FATTY ACID METABOLISM
2013-01-01 Eleonora Di Gregorio; Barbara Borroni; Elisa Giorgio; Daniela Lacerenza; Cecilia Mancini; Alessandro Calcia; Isabella Mura; Domenico Coviello; Nico Mitro; Marion Gaussen; Nicola Lo Buono; Ada Funaro; Giovanna Vaula; Isabelle Lagroua; Laura Orsi; Alexandra Durr; Chiara Costanzi; Alessandro Padovani; Alexis Brice; Loredana Boccone; Eriola Hoxha; Filippo Tempia; Donatella Caruso; Giovanni Stevanin; Alfredo Brusco
A NOVEL GENE FOR SPINOCEREBELLAR ATAXIA (SCA) LINKED TO CHROMOSOME 6 AND INVOLVED IN FATTY ACID METABOLISM
2013-01-01 Eleonora Di Gregorio; Barbara Borroni; Elisa Giorgio; Daniela Lacerenza; Cecilia Mancini; Alessandro Calcia; Isabella Mura; Domenico Coviello; Nico Mitro; Marion Gaussen; Nicola Lo Buono; Ada Funaro; Giovanna Vaula; Isabelle Lagroua; Laura Orsi; Alexandra Durr; Chiara Costanzi; Alessandro Padovani; Alexis Brice; Loredana Boccone; Eriola Hoxha; Filippo Tempia; Donatella Caruso; Giovanni Stevanin; Alfredo Brusco
A NOVEL GENE FOR SPINOCEREBELLAR ATAXIA (SCA) LINKED TO CHROMOSOME 6 AND INVOLVED IN FATTY ACID METABOLISM
2013-01-01 Eleonora Di Gregorio; Barbara Borroni; Elisa Giorgio; Daniela Lacerenza; Cecilia Mancini; Alessandro Calcia; Isabella Mura; Domenico Coviello; Nico Mitro; Marion Gaussen; Nicola Lo Buono; Ada Funaro; Giovanna Vaula; Isabelle Lagroua; Laura Orsi; Alexandra Durr; Chiara Costanzi; Alessandro Padovani; Alexis Brice; Loredana Boccone; Eriola Hoxha; Filippo Tempia; Donatella Caruso; Giovanni Stevanin; Alfredo Brusco
AFG3L2 mutations cause autosomal dominant ataxia SCA28 and reveal an essential role for the mitochondrial m-AAA protease complex in the cerebellum
2009-01-01 Di Bella D; Lazzaro F; Brusco A; Battaglia G; Pastore A; Finardi A; Fracasso V; Plumari M; Cagnoli C; Tempia F;Brussino A; Gellera C; Mariotti C; Pievani P;Di Donato S; Langer T; Muzi-Falconi M; Taroni F
AFG3L2 mutations cause autosomal dominant ataxia SCA28 and reveal an essential role of the m-AAA AGF3L2 homocomplex in the cerebellum
2008-01-01 DiBella D; Lazzaro F; Brusco A; Battaglia G; Pastore A; Finardi A; Fracasso V; Plumari M; Cagnoli C; Tempia F; Brussino A; Gellera C; Mariotti C; Pievani P; DiDonato S; Langer T; Muzi-Falconi M; Taroni F
Amyloid deposition during life span of APPPS1 mice, a murine model of Alzheimer's disease
2009-01-01 Montarolo F; Boda E; Hoxha E; Tempia F
Beta amyloid effects on cerebellar Purkinje cell excitability
2008-01-01 Hoxha E; Boda E; Montarolo F; Tempia F
Delayed motor learning and cerebellar electrophysiological alterations in a murine model of Alzheimer's disease with massive amyloidosis
2009-01-01 Hoxha E; Boda E; Montarolo F; Tempia F
Determinants of high frequency firing and discharge pattern modulation in cerebellar Purkinje cells
2004-01-01 Tempia F; Sacco T
Developmental time course of Kv3 voltage-gated potassium channels expression in mouse brain
2006-01-01 Boda E; Pini A; Tempia F
Effects of neuronal activity on intra- and extra-cellular beta amyloid in a transgenic murine model of Alzheimer’s disease
2011-01-01 Montarolo F; Parolisi R; Hoxha E; Tempia F
Expression pattern of the potassium channel accessory subunit Mirp2 in the mouse brain during development, in the adulthood and after lesion
2009-01-01 Boda E; Hoxha E; Montarolo F; Buffo A; Tempia F
Functional characterization of missense mutations in SCA28 patients, and development of a mouse model of the disease
2011-01-01 Mancini C; Roncaglia P; Stevanin G; Durr A; Brussino A; Cagnoli C; Krmac H; Limongi T; Montarolo F; Hoxha E; Turco E; Messana E; Altruda F; Gustincich S; Tempia F; Brusco A
GABAergic and excitability deficits in cerebellar Purkinje cells in APPPS1 mice, a murine model of Alzheimer's disease with massive amyloidosis
2009-01-01 Hoxha E; Boda E; Montarolo F; Parolisi R; Tempia F
Matrix Metalloproteinase-9 and PeriNeuronal Nets as New Therapeutic Targets for Fragile X Syndrome (FXS)
2025-01-01 Bertocchi Ilaria; Tempia Filippo; Hoxha Eriola; Oberto Alessandra; Luzzati Federico; Eva Carola; Nobile Veronica; Giuliani Lidia; Altieri Fabio; Tabolacci Elisabetta; Chiurazzi Pietro
Neurophysiology of locomotion: spinal mechanisms
2007-01-01 Tempia F
Reduced cerebellar Purkinje cell firing associated with motor impairment in Ebf2-null mice
2011-01-01 Hoxha E; Tonini R; Montarolo F; Croci L; Consalez GG; Tempia F
Spinocerebellar ataxia type 28: cellular and animal models to unravel the pathogenesis and to identify potential therapeutic targets
2015-01-01 CECILIA Mancini; ERIOLA Hoxha; EMILIA Turco; FIORELLA Altruda; FILIPPO Tempia; ALFREDO Brusco.
Studio dei meccanismi patogenetici dell’Atassia Spinocerebellare 28.
2012-01-01 Mancini C.; Roncaglia P.; Lo Buono N.; Gazzano E.; Brussino A.; Cagnoli C.; Krmac H.; Stevanin G.; Forlani S.; Hoxha E.; Funaro A.; Durr A.; Tempia F.; Altruda F.; Turco E.; Ghigo D.; Gustincich S.; Brusco A.
The GPR17 receptor participates in oligodendrocyte postnatal maturation and reaction to acute and chronic brain injury
2009-01-01 Boda E; Mantovan T; Rosa P; Tempia F; Abbracchio MP; Buffo A
| Titolo | Data di pubblicazione | Autore(i) | File |
|---|---|---|---|
| A NOVEL GENE FOR SPINOCEREBELLAR ATAXIA (SCA) LINKED TO CHROMOSOME 6 AND FATTY ACID METABOLISM | 2013 | Eleonora Di Gregorio; Barbara Borroni; Elisa Giorgio; Daniela Lacerenza; Cecilia Mancini; Alessandro Calcia; Isabella Mura; Domenico Coviello; Nico Mitro; Marion Gaussen; Nicola Lo Buono; Ada Funaro; Giovanna Vaula; Isabelle Lagroua; Laura Orsi; Alexandra Durr; Chiara Costanzi; Alessandro Padovani; Alexis Brice; Loredana Boccone; Eriola Hoxha; Filippo Tempia; Donatella Caruso; Giovanni Stevanin; Alfredo Brusco | |
| A NOVEL GENE FOR SPINOCEREBELLAR ATAXIA (SCA) LINKED TO CHROMOSOME 6 AND INVOLVED IN FATTY ACID METABOLISM | 2013 | Eleonora Di Gregorio; Barbara Borroni; Elisa Giorgio; Daniela Lacerenza; Cecilia Mancini; Alessandro Calcia; Isabella Mura; Domenico Coviello; Nico Mitro; Marion Gaussen; Nicola Lo Buono; Ada Funaro; Giovanna Vaula; Isabelle Lagroua; Laura Orsi; Alexandra Durr; Chiara Costanzi; Alessandro Padovani; Alexis Brice; Loredana Boccone; Eriola Hoxha; Filippo Tempia; Donatella Caruso; Giovanni Stevanin; Alfredo Brusco | |
| A NOVEL GENE FOR SPINOCEREBELLAR ATAXIA (SCA) LINKED TO CHROMOSOME 6 AND INVOLVED IN FATTY ACID METABOLISM | 2013 | Eleonora Di Gregorio; Barbara Borroni; Elisa Giorgio; Daniela Lacerenza; Cecilia Mancini; Alessandro Calcia; Isabella Mura; Domenico Coviello; Nico Mitro; Marion Gaussen; Nicola Lo Buono; Ada Funaro; Giovanna Vaula; Isabelle Lagroua; Laura Orsi; Alexandra Durr; Chiara Costanzi; Alessandro Padovani; Alexis Brice; Loredana Boccone; Eriola Hoxha; Filippo Tempia; Donatella Caruso; Giovanni Stevanin; Alfredo Brusco | |
| AFG3L2 mutations cause autosomal dominant ataxia SCA28 and reveal an essential role for the mitochondrial m-AAA protease complex in the cerebellum | 2009 | Di Bella D; Lazzaro F; Brusco A; Battaglia G; Pastore A; Finardi A; Fracasso V; Plumari M; Cagnoli C; Tempia F;Brussino A; Gellera C; Mariotti C; Pievani P;Di Donato S; Langer T; Muzi-Falconi M; Taroni F | |
| AFG3L2 mutations cause autosomal dominant ataxia SCA28 and reveal an essential role of the m-AAA AGF3L2 homocomplex in the cerebellum | 2008 | DiBella D; Lazzaro F; Brusco A; Battaglia G; Pastore A; Finardi A; Fracasso V; Plumari M; Cagnoli C; Tempia F; Brussino A; Gellera C; Mariotti C; Pievani P; DiDonato S; Langer T; Muzi-Falconi M; Taroni F | |
| Amyloid deposition during life span of APPPS1 mice, a murine model of Alzheimer's disease | 2009 | Montarolo F; Boda E; Hoxha E; Tempia F | |
| Beta amyloid effects on cerebellar Purkinje cell excitability | 2008 | Hoxha E; Boda E; Montarolo F; Tempia F | |
| Delayed motor learning and cerebellar electrophysiological alterations in a murine model of Alzheimer's disease with massive amyloidosis | 2009 | Hoxha E; Boda E; Montarolo F; Tempia F | |
| Determinants of high frequency firing and discharge pattern modulation in cerebellar Purkinje cells | 2004 | Tempia F; Sacco T | |
| Developmental time course of Kv3 voltage-gated potassium channels expression in mouse brain | 2006 | Boda E; Pini A; Tempia F | |
| Effects of neuronal activity on intra- and extra-cellular beta amyloid in a transgenic murine model of Alzheimer’s disease | 2011 | Montarolo F; Parolisi R; Hoxha E; Tempia F | |
| Expression pattern of the potassium channel accessory subunit Mirp2 in the mouse brain during development, in the adulthood and after lesion | 2009 | Boda E; Hoxha E; Montarolo F; Buffo A; Tempia F | |
| Functional characterization of missense mutations in SCA28 patients, and development of a mouse model of the disease | 2011 | Mancini C; Roncaglia P; Stevanin G; Durr A; Brussino A; Cagnoli C; Krmac H; Limongi T; Montarolo F; Hoxha E; Turco E; Messana E; Altruda F; Gustincich S; Tempia F; Brusco A | |
| GABAergic and excitability deficits in cerebellar Purkinje cells in APPPS1 mice, a murine model of Alzheimer's disease with massive amyloidosis | 2009 | Hoxha E; Boda E; Montarolo F; Parolisi R; Tempia F | |
| Matrix Metalloproteinase-9 and PeriNeuronal Nets as New Therapeutic Targets for Fragile X Syndrome (FXS) | 2025 | Bertocchi Ilaria; Tempia Filippo; Hoxha Eriola; Oberto Alessandra; Luzzati Federico; Eva Carola; Nobile Veronica; Giuliani Lidia; Altieri Fabio; Tabolacci Elisabetta; Chiurazzi Pietro | |
| Neurophysiology of locomotion: spinal mechanisms | 2007 | Tempia F | |
| Reduced cerebellar Purkinje cell firing associated with motor impairment in Ebf2-null mice | 2011 | Hoxha E; Tonini R; Montarolo F; Croci L; Consalez GG; Tempia F | |
| Spinocerebellar ataxia type 28: cellular and animal models to unravel the pathogenesis and to identify potential therapeutic targets | 2015 | CECILIA Mancini; ERIOLA Hoxha; EMILIA Turco; FIORELLA Altruda; FILIPPO Tempia; ALFREDO Brusco. | |
| Studio dei meccanismi patogenetici dell’Atassia Spinocerebellare 28. | 2012 | Mancini C.; Roncaglia P.; Lo Buono N.; Gazzano E.; Brussino A.; Cagnoli C.; Krmac H.; Stevanin G.; Forlani S.; Hoxha E.; Funaro A.; Durr A.; Tempia F.; Altruda F.; Turco E.; Ghigo D.; Gustincich S.; Brusco A. | |
| The GPR17 receptor participates in oligodendrocyte postnatal maturation and reaction to acute and chronic brain injury | 2009 | Boda E; Mantovan T; Rosa P; Tempia F; Abbracchio MP; Buffo A |